Physiology and Anatomy

Dandy-walker syndrome is a rare disorder characterizsed by complete or partial agenesis of the vermis, cystic dilatation of the fourth ventricule and an enlarged posterior fossa. The precise aetiology is unknown, although there have been reports of associations with risk factors like maternal virus infections (rubella, toxoplasma and cytomegalovirus) and alcohol consumtion [1]. It describe a rare case of five months old boy with acute respiratory distress with the exploration objective a Dandy-walker syndrome.A five months old boy with no medical history was admitted to the intensive unity care fot an acute rispiratory distress, the exploration of the respiratory distress lead as to realising a cerebral CT scan which objictived dilatation of the ventricular system and enlargement of the fourth ventricular and vermin hypoplasia related to Dandy-walker syndrome.A dandy walker is a rare condition and the image found may not be the cause of the acute respiratory distress. Clinical presentation and prognosis depends on the prenatal and early diagnostic dering the first year of live and the treatement is surgical

Leiomyoma of the urethra is a rare benign tumor composed of smooth muscle tissue often overlooked by most practitioners. This tumor results in a variety of clinical signs, diagnosis is histological. This pathology can generates significant repercussions on the social life of the patient.

Mycotic aneurysms are a uncommon presentation may be with rupture or sepsis. Disease management is often required to prevent catastrophic complications .Bacterial endocarditis is one of the classic causes of infected aneurysm. We report a case of a 14 8 mm mycotics plenics artery aneurysm secondary to endocarditis. Our patient have aortic and mitral valve replacements for acute articular Rheumatism, the disease management for our patient is a active surveillance of the aneurysm without complications. Our methodology is to review english and frensh articles from PubMed and cochran.

We reported a case of a 61-year-old patient, operated in 2005 for renal calculus, was received consultation for abdominal pain, clinical examination found a mass of the right flank, MRI found a large mass of the right flank coarsely limited rounded enclosures and surrounded by a thin wall evoking a carcinoma or cystic lymphangioma. The anatomopathological examination of the piece made the diagnosis of a foreign body evoking a Textilome.

Patients withbladderexstrophy have a higherrisk of bladder cancer, usuallyadenocarcinomakind . The squamouscellcarcinomais rare, withonly 12 cases reported in the literature. We report one case of squamouscellcarcinoma of bladderexstrophyoccursunrepairedchild in a 34 yearsold man.

Evaluate retrospectively, in a homogeneous series of patients with synovial sarcoma of the limbs, the different steps of the management of this disease, the diagnosis and the therapeutic difficulties. This is a retrospective study of 20 cases of synovial sarcoma of the limbs treated in orthopedic surgery department at Ibn Sina university hospital and in the National Institute of Oncology Rabat, between January 2000 and December 2012. 20 cases of synovial sarcoma of the limbs were collected of which 12 were localized in the lower limb and 8 localized in the upper limb. The mean age was 45 years with a male predominance. The patients consulted after an average period of 18 months and tumoral syndrome was the constant reason for consultation. All the patients were treated surgically, except the 4 cases with lung metastases. After an average follow-up of 48 months, 10 patients are alive, 5 died and 5 are lost of view. Because of their rarity, the diversity of their histological types and their localization, synovial sarcoma presents problems at every stage of their management. Identification of specific chromosomal translocations is a great advantage in their diagnosis. Multidisciplinary approach is mandatory in their management.

Myocarditis is an inflammatory disease of the cardiac muscle associated with both infectious and noninfectious diseases. Among the infectious etiologies, viruses are the most frequent pathogens, streptococcus is rarely reported as a causative pathogen of acute myocarditis without clinical features suggestive of rheumatic fever. No epidemiological data estimating the incidence of group A streptococcus (GAS) induced myocarditis exist at this time [1]. The clinical manifestations are variable: it classically presents as an acute heart failure and can also be manifested with arrhythmia (tachycardia or bradycardia) or chest pain mimicking myocardial infarction, especially in young patients, accompanied with focal ST elevations on the electrocardiogram and elevated cardiac biomarkers. Here we present a case of a 44- year-old man who presented with myocarditis mimicking ST elevation myocardial infarction (STEMI) a few days after he an episode of angina.

The urinary bilharziasis are parasitic affections whose pathogenic agent is Schistosoma. Only the urogenital schistosomiasis due to the species S. haematobium exists in Morocco. The testicular sites of bilharziomas are rare. We report an interesting case of epididymal bilharziasis in a young man with only apparently benign nodules of the testes on imaging.

a 60-year-old woman,with a medical history of high blood pressure ,had an autosomal dominant polycystic kidney disease (ADPKD) with end-stage renal disease under regular peritoneal dialysis since January 2014. The patient presented to our institution with right flank pain and gross hematuria , physical examination was unremarkable . laboratory examination revealed a normocystic anemia with a hemoglobin at 10,6 g/dL ,. Platelet and white blood cellas count were normal , her serum creatinin was 85,5 mg/l . Urinalysis showed microscopic hematuria and no infection .

We report a case of Fisher/guillainbarré overlap in a 14 years old patient with antecedent of an infectious respiratory event one week before the installation of Miller fisher Syndrome. The symptomatology rapidly evolved into a case of guillainbarré with respiratory and deglutition disorders. The patient received 2 courses of IvIg, 5 days each, with a 2 weeks interval which resulted in a total decline of paralysis and motor recovery. This case shows the importance of meticulous surveillance of patients with Miller Fisher syndrome in order to act on first symptoms of a guillainbarré overlap.